Langerhans cell histiocytosis of the ear

نویسندگان

  • Usama M Rashad
  • Hussein Awad Ali
  • Mahmoud R. Hussein
  • Mahmoud R. A. Hussein
چکیده

Langerhans cell histiocytosis (LCH) is a rare neoplastic lesion characterized by accumulation of cells having major phenotypic features of skin Langerhans cells. It usually affects young children but rare cases were also reported in adults. The clinical spectrum of LCH includes Letterer–Siwe disease, Hand–Schüller–Christian disease, eosinophilic granuloma, Langerhans cell sarcoma as well as intermediate and poorly elucidated forms. Here we address the clinicopathologic features and histogenesis of this condition.

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تاریخ انتشار 2017